COVID-19 (Coronavirus) Information

Your health and safety are our top priorities. Learn more about our COVID-19 evaluation and testing and our commitment to providing great care while maintaining the safest environment possible.

Health Library

Aortic arch syndrome
     
Print-Friendly
Bookmarks

Aortic arch syndrome

Subclavian artery occlusive syndrome; Carotid artery occlusion syndrome; Subclavian steal syndrome; Vertebral-basilar artery occlusive syndrome; Takayasu disease; Pulseless disease

 

The aortic arch is the top part of the main artery carrying blood away from the heart. Aortic arch syndrome refers to a group of signs and symptoms associated with structural problems in the arteries that branch off the aortic arch.

 

Causes

 

Aortic arch syndrome problems can be due to trauma, blood clots, or malformations that develop before birth. These defects result in abnormal blood flow to the head, neck, or arms.

In children, there are many types of aortic arch syndromes, including:

  • Congenital absence of a branch of the aorta
  • Isolation of the subclavian arteries
  • Vascular rings

An inflammatory disease called Takayasu syndrome may result in narrowing (stenosis) of the vessels of the aortic arch. This typically occurs in women and girls. This disease is seen more often in people of Asian descent.

 

Symptoms

 

Symptoms vary according to which artery or other structure that has been affected. Symptoms may include:

  • Blood pressure changes
  • Breathing problems
  • Dizziness, blurred vision, weakness, and other brain and nervous system (neurological) changes
  • Numbness of an arm
  • Reduced pulse
  • Swallowing problems
  • Transient ischemic attacks (TIA)

 

Treatment

 

Surgery is often needed to treat the underlying cause of aortic arch syndrome.

 

 

References

Braverman AC, Schermerhorn M. Diseases of the aorta. In: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Braunwald's Heart Disease: A Textbook of Cardiovascular Medicine. 11th ed. Philadelphia, PA: Elsevier; 2019:chap 63.

James WD, Elston DM, Treat JR, Rosenbach MA, Neuhaus IM. Cutaneous vascular diseases. In: James WD, Elston DM, Treat JR, Rosenbach MA, Neuhaus IM, eds. Andrews' Diseases of the Skin: Clinical Dermatology. 13th ed. Philadelphia, PA: Elsevier; 2020:chap 35.

Langford CA. Takayasu arteritis. In: Hochberg MC, Gravallese EM, Silman AJ, Smolen JS, Weinblatt ME, Weisman MH, eds. Rheumatology. 7th ed. Philadelphia, PA: Elsevier; 2019:chap 165.

BACK TO TOPText only

 
  • Heartbeat

    Heartbeat

    Animation

  • Heart - section through the middle

    Heart - section through the middle

    illustration

  • Vascular ring

    Vascular ring

    illustration

  • Heartbeat

    Animation

  • Heart - section through the middle

    Heart - section through the middle

    illustration

  • Vascular ring

    Vascular ring

    illustration

A Closer Look

 

Talking to your MD

 

    Self Care

     

      Tests for Aortic arch syndrome

       
       

      Review Date: 4/30/2020

      Reviewed By: Thomas S. Metkus, MD, Assistant Professor of Medicine and Surgery, Johns Hopkins University School of Medicine, Baltimore, MD. Also reviewed by David Zieve, MD, MHA, Medical Director, Brenda Conaway, Editorial Director, and the A.D.A.M. Editorial team.

      The information provided herein should not be used during any medical emergency or for the diagnosis or treatment of any medical condition. A licensed medical professional should be consulted for diagnosis and treatment of any and all medical conditions. Links to other sites are provided for information only -- they do not constitute endorsements of those other sites. © 1997- A.D.A.M., a business unit of Ebix, Inc. Any duplication or distribution of the information contained herein is strictly prohibited.
      adam.com